Abstract

Congenital cystic adenomatoid malformation (CCAM) is a rare congenital disorder of pulmonary development that usually presenting as a respiratory distress in the neonatal period. Presentation in adulthood is rare and only 40 cases of CCAM in adulthood have been reported in literatures. A 49-year-old woman presented with hemoptysis. Postero anterior chest radiograph showed an air-fluid level in right upper lobe. A computed tomographic (CT) scan of the chest showed multilocular thick-walled cystic lesions in right upper lobe. A CT angiography showed cystic lesions with normal bronchial artery supply in right upper lobe, which were consistent with CCAM. A complete surgical resection of the right upper lobe was performed confirming a type 2 CCAM according to the expanded Stocker's classification.

• Keywords: Congenital cystic adenomatoid malformation;Congenital malformation;